9. A 20-year-old white male with a long standing history of epilepsy was found dead face down in his bedroom. The relatives of the deceased stated that his condition worsened recently. The seizures became more frequent and were poorly controlled despite adjustment of medications. An autopsy was performed at Medical Examiner’s office. The external examination of the body revealed multiple, firm, brown, telangiectatic papules located in the nasolabial folds, chin, and cheeks (see gross image). The areas of thick leathery skin resembling an orange peel were found on the lower back and posterior neck. Examination of formalin-fixed brain revealed expanded, pale and firm gyri in both frontal and parietal lobes (see gross images below).
Sectioning of the formalin fixed brain also showed well-demarcated, multinodular masses of fleshy, gray– pink tissue in the wall of the lateral ventricles. Cut surface of the lesions displayed foci of calcification. Gross and microscopic images are provided below.
All the statements about this lesion are true EXCEPT: